(01)갈락토스-1-인산 Galactose-1-Phosphate
(02)갈락토스-1-인산우리딜 전달효소 Galactose-1-Phosphate Uridyltransferase
(03)갈락토키나아제
(04)베타갈락토시다제 β-Galactosidase
(05)아릴설파타제 A Arylsulfatase A
(06)아릴설파타제 B Arylsulfatase B
(07)알파갈락토시다제 α-Galactosidase
(08)에시드알파글루코시다제 Acid-α-Glucosidase
(09)우리딘이인산갈락토스- 4-에피머라아제 Uridine Diphosphate (UDP) Galactose-4- Epimerase
(10)알파엔아세틸글루코사미니다제 α-N-Acetylglucosaminidase (NAGLU)
(11)알파글루코사민 엔-아세틸트랜스페라제 α-Glucosamine N-acetyltransferase
(12)베타글루쿠로니다제 β-Glucuronidase
(13)베타글루코세레브로시다제 β-Glucocerebrosidase
(14)베타헥소사미니다제 β-Hexosaminidase
(15)알파엘-퓨코시다제 α-L-Fucosidase
(16)알파만노시다제 α-Mannosidase
(17)베타만노시다제 β-Mannosidase
(18)비오티니다제 Biotinidase